Unilateral Agenesis of Pulmonary Artery

Gulfidan Cakmak, Nurdan Gocgun, Emre Evren, Zuhal Aydan Saglam

Abstract


Isolated unilateral agenesis of pulmonary artery was first defined at 1868. Although the exact prevalance is unknown, in a study it is estimated as 1/200,000. Congenital unilateral agenesis of pulmonary artery is a rare anomaly which is frequently associated with other congenital cardiovascular anomalies such as tetralogy of Fallot or septal defects. In 37% of cases left pulmonary artery is absent while in 63% the right one is absent. Nearly 30% of patients are asymptomatic. When symptomatic, patients may experience chest pain, pleural effusion, recurrent pulmonary infections, dyspnea or limited exertion or hemoptysis. Several methods are used in diagnosis such as computerized tomography, bronchography, perfusion scintigraphy, echocardiography and cardiac catheterisation. Massive hemoptysis, cardiac insufficiency, bronchectasis and necrotizing bronchopnemonia may be included among the complications. The following case report presents a patient who was not diagnosed until adult ages.




J Med Cases. 2013;4(10):696-698
doi: http://dx.doi.org/10.4021/jmc1428w

Keywords


Congenital pulmonary disease; Pulmonary artery agenesis; Pulmonary artery disease

Full Text: HTML PDF
 

Browse  Journals  

 

Journal of Clinical Medicine Research

Journal of Endocrinology and Metabolism

Journal of Clinical Gynecology and Obstetrics

 

World Journal of Oncology

Gastroenterology Research

Journal of Hematology

 

Journal of Medical Cases

Journal of Current Surgery

Clinical Infection and Immunity

 

Cardiology Research

World Journal of Nephrology and Urology

Cellular and Molecular Medicine Research

 

Journal of Neurology Research

International Journal of Clinical Pediatrics

 

 
       
 

Journal of Medical Cases, monthly, ISSN 1923-4155 (print), 1923-4163 (online), published by Elmer Press Inc.                     
The content of this site is intended for health care professionals.
This is an open-access journal distributed under the terms of the Creative Commons Attribution-NonCommercial 4.0 International License, which permits unrestricted
non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.
Creative Commons Attribution license (Attribution-NonCommercial 4.0 International CC-BY-NC 4.0)


This journal follows the International Committee of Medical Journal Editors (ICMJE) recommendations for manuscripts submitted to biomedical journals,
the Committee on Publication Ethics (COPE) guidelines, and the Principles of Transparency and Best Practice in Scholarly Publishing.

website: www.journalmc.org   editorial contact: editor@journalmc.org
Address: 9225 Leslie Street, Suite 201, Richmond Hill, Ontario, L4B 3H6, Canada

© Elmer Press Inc. All Rights Reserved.