Journal of Medical Cases, ISSN 1923-4155 print, 1923-4163 online, Open Access
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Case Report

Volume 6, Number 5, May 2015, pages 221-225

Perioperative Care of an Adolescent With 11-Beta-Hydroxylase Deficiency


Table 1. Previous Reports of Anesthesia in Patients With Congenital Adrenal Hyperplasia
Author and referencePatient ageHyperglycemiaHypertensionCo-morbid conditionsMedicationsLab resultsSurgical procedureAnestheticIntraoperative problems
MPS: mucopolysaccharoidosis; GA: general anesthesia; LMA: laryngeal mask airway; TIVA: total intravenous anesthesia; DMD: Duchenne muscular dystrophy; sBP: systolic blood pressure.
Bansal et al [28]3 yearsNoNoMaroteaux-Lamy disease (MPS IV)Hydrocortisone 10 mg/day, prednisolone 1.5 mg/dayNormalMRI of the brainGeneral inhalational anesthesia with sevoflurane using an LMANone
Okamoto et al [29]12 yearsNoYes, severeNoneSpironolactone (dose unspecified)Not reportedGenitoplastyGeneral inhalational anesthesia with nitrous oxide and sevoflurane; epidural catheterSevere hypertension (sBP > 180 mm Hg)
Van Obbergh et al [30]6 yearsNoNoXp21 deletion, DMD, glycerol kinase deficiencyHydrocortisone (dose unspecified)Not reportedBilateral hip osteotomiesTIVA with remifentanil, bolus doses of thiopentone and endotracheal intubation, epidural catheterNone
Yamashita [31]8 weeksNoNoNoneHydrocortisone 15 mg twice a dayPotassium 5.6 mmol/L, sodium 132 mmol/LGenitoplastyChloral hydrate, spinal anesthesia with tetracaineNone