Journal of Medical Cases, ISSN 1923-4155 print, 1923-4163 online, Open Access
Article copyright, the authors; Journal compilation copyright, J Med Cases and Elmer Press Inc
Journal website http://www.journalmc.org

Case Report

Volume 4, Number 5, May 2013, pages 340-344


STILL out of Breath?

Tables

Table 1. Yamaguchi Criterion for Adult Onset Still’s Disease*
 
* 5 criterions needed, with a minimum of 2 major; **ANA: Antinuclear antibody, RF: Rheumatoid factor.
Major criteria
  Fever ≥ 39 °C, lasting ≥ 1 week
  Arthralgia, lasting ≥ 2 weeks
  Non-pruritic, salmon colored macular or maculopapular rash
  Leukocytosis ≥ 10 000/µL, with 80% granulocytes
Minor criteria
  Sore throat
  Lymphadenopathy
  Hepatomegaly or splenomegaly
  Liver enzymes elevation
  Negative ANA and RF**

 

Table 2. WHO Classification of Pulmonary Artery Hypertension (PAH)
 
Group 1 PAH: pulmonary arterial hypertension
  Sporadic PAH
  Familial PAH
  PAH associated with small arteriolar diseases (collagen vascular disease, anorexigens, HIV, etc)
Group 2 PAH: pulmonary venous hypertension
  Mainly left heart disease
Group 3 PAH: PAH associated with respiratory system disorder
  Sleep apnea
  Interstitial lung diseases
  Chronic obstructive pulmonary disease
Group 4 PAH: PAH associated with thrombotic disorders
  Thrombotic occlusion of pulmonary arteries (pulmonary embolisms)
  Non-thrombotic occlusion of pulmonary arteries (Katayama disease seen with schistosomiasis)
Group 5 PAH: PAH of extrinsic nature
  Mechanical compression of pulmonary vasculature (sarcoidosis, histiocytosis, etc)