| Journal of Medical Cases, ISSN 1923-4155 print, 1923-4163 online, Open Access |
| Article copyright, the authors; Journal compilation copyright, J Med Cases and Elmer Press Inc |
| Journal website http://www.journalmc.org |
Case Report
Volume 6, Number 5, May 2015, pages 221-225
Perioperative Care of an Adolescent With 11-Beta-Hydroxylase Deficiency
Table
| Author and reference | Patient age | Hyperglycemia | Hypertension | Co-morbid conditions | Medications | Lab results | Surgical procedure | Anesthetic | Intraoperative problems |
|---|---|---|---|---|---|---|---|---|---|
| MPS: mucopolysaccharoidosis; GA: general anesthesia; LMA: laryngeal mask airway; TIVA: total intravenous anesthesia; DMD: Duchenne muscular dystrophy; sBP: systolic blood pressure. | |||||||||
| Bansal et al [28] | 3 years | No | No | Maroteaux-Lamy disease (MPS IV) | Hydrocortisone 10 mg/day, prednisolone 1.5 mg/day | Normal | MRI of the brain | General inhalational anesthesia with sevoflurane using an LMA | None |
| Okamoto et al [29] | 12 years | No | Yes, severe | None | Spironolactone (dose unspecified) | Not reported | Genitoplasty | General inhalational anesthesia with nitrous oxide and sevoflurane; epidural catheter | Severe hypertension (sBP > 180 mm Hg) |
| Van Obbergh et al [30] | 6 years | No | No | Xp21 deletion, DMD, glycerol kinase deficiency | Hydrocortisone (dose unspecified) | Not reported | Bilateral hip osteotomies | TIVA with remifentanil, bolus doses of thiopentone and endotracheal intubation, epidural catheter | None |
| Yamashita [31] | 8 weeks | No | No | None | Hydrocortisone 15 mg twice a day | Potassium 5.6 mmol/L, sodium 132 mmol/L | Genitoplasty | Chloral hydrate, spinal anesthesia with tetracaine | None |